Midface advancement in an adult patient with Crouzon syndrome: Modified LeFort III + LeFort I osteotomy accompanied by genioplasty and nasal dorsum augmentation

Abstract

Crouzon syndrome is an autosomal dominant trait, leading to midface deficiency, undeveloped
orbits, short nasal dorsum, and exophthalmos as the typical clinical features. Early correction
of craniofacial problems can improve patients’ quality of life, but many of these patients with
Crouzon syndrome are seeking treatment in older ages when they are missed for multidisciplinary
management and distraction technique in proper timing. Modified LeFort III osteotomy is one of
the treatment options that can be used for proper resolution in adult patients. The present case
report study aims to describe a patient with midface deficiency due to the Crouzon syndrome
who has undergone a combination of modified LeFort III osteotomy with the periocular approach
and LeFort I osteotomy, nasal dorsum augmentation accompanied by genioplasty, wholly as a single
surgical procedure which has been shown that can result in highly satisfactory outcomes for both
patient and surgeon.
Key Words: Craniofacial dysostosis, Crouzon syndrome, midface advancement, midface
hypoplasia, modified LeFort iii osteotomy